Glycogen Storage Diseases Carbohydrate metabolism provides energy for meta­bolic functions of cell. Metabolism of glucose generates ATP by glycolysis and oxidative phosphorylation. Any one of several heritable diseases characterized by the abnormal storage and accumulation of glycogen in the tissues, esp. in the liver Dietary sources of glucose: · Polysaccharide...
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Sarcoidosis It is a chronic, multisystem disorder of unknown cause. chronic multisystem disease of unknown etiology, characterized by noncaseating (hard) granulomas and lymphocytic alveol, Sarcoidosis is a noninfectious, multisystem granulomatous disease of unknown cause, commonly affecting young and middle-aged adults. Almost any other organ may be involved, including liver, spleen,...
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Sepsis (Septic Shock) Prognosis Prevention TREATMENT TREATMENT Sepsis (Septic Shock) Admit in ICU Treat local site of infection Monitor hemodynamics. Sepsis is a clinical syndrome characterized by systemic inflammation due to infection. There is a continuum of severity ranging from sepsis to severe sepsis and septic shock. Antimicrobial therapy in...
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Ostium Primum ASD (Inter atrial communica­tion) The opening in the first septum of the embryonic heart; it closes as the ventricles form. There is right to left shunt and mitral valve regurgita­tion. Symptoms occur in childhood itself with congestive heart failure and retarded growth and development. There is atrial fibrillation...
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CONGENITAL HEART DISEASES General defects structural problem in the heart  Acyanotic congenital heart diseases with nor­mal or decreased pulmonary arterial blood flow (no shunt). Left sided HEART Malformations or structural problem in the heart  Cardiac mal positions – Dextrocardia etc. Congenitally corrected transposition of great ar­teries .(CTGA). Coarctation of aorta Mitral...
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