CONGENITAL HEART DISEASES General HEART Malformations defects or structural problem

CONGENITAL HEART DISEASES General defects structural problem in the heart 

Acyanotic congenital heart diseases with nor­mal or decreased pulmonary arterial blood flow (no shunt). Left sided HEART Malformations or structural problem in the heart 

    • Cardiac mal positions – Dextrocardia etc.
    • Congenitally corrected transposition of great ar­teries .(CTGA).
  • Coarctation of aorta
  • Mitral stenosis.
  • Mitral regurgitation
  • Obstruction at left atrium
  • Pulmonary vein stenosis
  • Cor triatriatum
  • Endocardial cushion defect – Abnormal mitral valve (ASD + MR or ostium primum defect).
  • Congenitally corrected transposition of great arteries.
  • Congenital perforation, accessory commis­sure, chordae defects, cleft posterior leaflet.
  • valvular.
  • Aortic regurgitation.
  • Primary endocardial fibroelastosis.
  • Aortic stenosis – Subvalvular, Valvular, Supra-
CONGENITAL HEART DISEASES 1
CONGENITAL HEART DISEASES General defects structural

Right Sided HEART Malformations or structural problem in the heart 

  • Ebstein’s anomaly of TV (ac anotic tw~).
  • Pulmonary stenosis – Subinfundibular, Infundibu­lar, Valvular, Supravalvular.
  • Idiopathic dilatation of the pulmonary artery (IDPA).

cyanotic congenital heart disease with in­creased pulmonary arterial blood flow (left to right shunt)

  • Atrial Shunt
  • ASD
  • Sinus venosus defect – small, high de fect
  • Partial anomalous pulmonary venous connec­tion (PAPVC).
  • Ostium secundum – Simple ASD
  • Ostium primum – ASD with MR
  • ASD with mitral stenosis (Lutembacher’s syn­drome)- (Congenital ASD with rheumatic MSJ

Ventricular shunt

  • VSD
  • VSD with Aortic regurgitation

 Shunt between aortic root and right side of heart

  • Coronary arteriovenous fistula.
  • Ruptured sinus of Valsalva Aneurysm.

Shunt at aortopulmonary level  

  • Patent ductus arteriosus.
  • Aorto-pulmonary window.
  • Anomalous origin of coronary artery from pulmonary trunk.
  • Complete common Atrioventricular Canal (atrioventricular septal defect)

Cyanotic congenital heart diseases

  • Increased pulmonary arterial blood flow (PABF)
  • Corrected Transposition of Great Arteries (CTGA)
  • Total anomalous pulmonary venous connection
  • (TAPVC)
  • Univentricular heart (no PS)
  • Taussig Bing Anomaly
  • Truncus arteriosus

Decreased pulmonary arterial blood flow or Nor­mal PABF

  • Dominant LV
  • Total anomalous pulmonary venous connec­tion.
  • Pulmonary atresia with intact ventricular sep­tum.
  • Ebstein’s anomaly of TV
  • Single LV with PS.
  • Dominant RV decreased PABF) No Pulmonary Hypertension , Fallot’s tetralogy
  • PS with ASD
  • PS with CTGA
  • DORV with PS (Double outlet right ventricle
  • with Pulmonary stenosis).
  • With Pulmonary hypertension (Eisenmengers syndrome)
  • Total anomalous pulmonary venous connec­tion with pulmonary hypertension.
  • Aortic atresia, mitral atresia (hypoplastic left heart)
  • Normal ventricles
  • Pulmonary AV fistula
  • Vena cava – left atrium communication
  • Atrial septal defect with reversed shunt – right to left shunt.
  • Ventricular septal defect with reversed shunt­right to left shunt.
  • Patent ductus arteriosus or aortic pulmonary window with reversed shunt .
  • Double outlet right ventricle with pulmonary hypertension.
  • Corrected transposition of great arteries with pulmonary hypertension .
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